For those of you who may be interested!  In an attempt to update information I offer 
to Families today I had a lenghty discussion with a chap from the Neonatal Screening 
Department in Brisbane.  My intention was for some accurate statistics of the 
"routinely" tested metabolic disorders in Queensland.  Responses of some questions 
asked.....

PKU- 1:12 5000
Hereditary- parents will have PKU or be carriers.  1:4 if a parent  has PKU.

Congenital hypothryroidism- 1:3 500
Hereditary or occurs naturally no known stats for individual occurrance.
Clinical manisfestation of cretinism if newborn affected  usually manifest 1-2 wks 
"may have irreviserable damage by then".  Dept tells me they have notified parents by 
day 7 if NNST performed.  Antithyroid drugs may induce congenital hypothyroidism.  (? 
this factor grouped in natural occurance ??  no stats available)

Cystic fibrosis- 1:3 000
Purely hereditary "most commonly affects newborns of caucasian desent".  Both parents 
must be carriers if either parent is not affected by CF.  No individual stats 
available for a parent affected or carrier transfer.

Galactosaemia- 1:34 000
Hereditary.  Females affected are usually infertile.  A Woman may be a carrier, both 
parents must be carriers for a newborn to be affected.  Most carriers or peoples 
affected  experience intelluctual impairement (known suffers identifiable).   
Classical galactosaemia if untreated life expectance 2-3wks usually manifests as 
sepsis @ 1 week of age if diagnosed and diet modification "not expected to die" but 
degrees of intelluctual impairement expected also severe hepatic dysfunction and GI 
problems with life long diet modification.  Nil differentiation between B/F and A/F.

I am expecting some literature to be posted if anything remarkable will let you know.

cheers
Katrina

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